Idiopathic pulmonary fibrosis (IPF)

What’s Your Rare iQ?

In what country is the prevalence of Behcet's disease the highest?

Activated PI3K delta syndrome (APDS)

Rare View

60% of tuberous sclerosis cases are diagnosed in the first year. Diagnosis slows down considerably after the first year.

Measured by: prevalence

Disease	Est US Prevalence	Inheritance	Age of onset
Sarcoidosis	66,000-158,600
Chronic thromboembolic pulmonary hypertension	20,970-82,000
Granulomatosis with Polyangiitis (Wegener's)	9,200-30,000
Granulomatosis with polyangiitis (Churg-Strauss)	3,630-8,000
Idiopathic pulmonary fibrosis (IPF)	62,000-140,100
Behcet's disease	9,000-17,200
Alpha-1 Antitrypsin Deficiency	60,000-100,000
Cystic fibrosis	30,000-35,000
Pulmonary arterial hypertension (PAH)	8,900-52,800
Idiopathic Interstitial pneumonias	60,000-125,000
Tuberculosis	8,580-34,970








Pulmonary Alveolar Proteinosis (PAP) Syndrome
Lymphangioleiomyomatosis (LAM)
Birt-Hogg-Dubé syndrome (BHD)
Pulmonary Langerhans cell histiocytosis (PLCH)
Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH)
Pulmonary alveolar microlithiasis (PAM)
Lymphangiomatosis or generalized lymphatic anomaly (GLA-now the preferred name)